Endolymphatic Sac Tumor of The Temporal Bone-Juniper Publishers

 Juniper Publishers-Open Access Journal of Head Neck & Spine Surgery

Endolymphatic Sac Tumor of The Temporal Bone

Authored by Behzad Saberi

Keywords: Endolymphatic sac tumor; Temporal bone

Opinion

Endolymphatic sac tumor of the temporal bone is a locally aggressive tumor which involves the sac and the endolymphatic duct. From the histological point of view, endolymphatic sac tumor can be described as a destructive papillary cystic adenomatous tumor. It can be sporadic or related to the von Hippel-Lindau disease. Chromosome 3p25 tumor suppressor gene’s loss of function can cause von Hippel-Lindau which the patients with von Hippel-Lindau disease may have bilateral endolymphatic sac tumors. So, it is advisable to screen the patients with von Hippel-Lindau disease for the presence of bilateral endolymphatic sac tumors.

Patients with endolymphatic sac tumors can be presented with various symptoms like aural fullness, sensorineural hearing loss, vertigo and tinnitus which seemingly are due to endolymph’s normal flow and resorption patterns obstruction which may cause endolymphatic hydrops. Lower cranial neuropathies, facial paralysis and brainstem compression symptoms can be seen in the late phases of the disease. Imaging studies of the patients with endolymphatic sac tumors can include MRI and CT. In comparison with the cerebellar white matter, the tumor can be isointense to hyperintense in T1 MRI imaging. If T1 would be done with contrast, the tumor will become strongly enhancing. In T2, the tumor would be heterogeneous, and it is because of the highly vascular nature of the tumor. Posterior fossa plate’s bony destruction in addition to central calcifications which may also have extension to the mastoid can be seen in the CT.

The treatment for the patients with endolymphatic sac tumor would be done by surgery. During surgery, both dural surfaces should be removed so that the goal of complete removal of the tumor can be achieved. Preoperative embolization should be done in large tumors so that the amounts of blood loss can be minimized as much as possible. In the cases which hearing sparing would not be the goal, translabyrinthine approach would be the surgical choice while retrolabyrinthine and transdural approaches are the surgical options for the cases with small tumors which hearing sparing would be the goal.

For more articles in Open access Journal of Head Neck & Spine Surgery | please click on: https://juniperpublishers.com/jhnss/index.php

For more about Juniper Publishers | please click on: https://juniperpublishers.com/pdf/Peer-Review-System.pdf

Comments

Post a Comment

Popular posts from this blog

Parapharyngeal Space Tumors - "A Surgical Challenge"-Juniper publishers

Image
JUNIPER PUBLISHERS-OPEN ACCESS JOURNAL OF HEAD NECK & SPINE SURGERY Abstract Parapharyngeal space tumors are rare entity. Overall incidence is less than 0.5%. These tumors are divided into prestyloid and post styloid tumors. Salivary gland neoplasma are common in prestyloid compartment whereas Neurogenic tumors in post styloid compartment. As these tumors are painless and does not express signs and symptoms at early stage, diagnosis of such tumors needs critical evaluation. Anatomic complexity of PPS makes surgical excision more challenging. We have reported 4 cases of parapharyngeal space tumors over a period of 10 years. Keywords: Parapharyngeal; Schwannoma; Paraganglioma; Neurogenic; Transcervical Background Parapharyngeal space is an inverted pyramid from base of the skull to hyoid bone. It is bounded medially by pharynx, anteriorly pterygomandibular raphe, posterolaterally carotid sheath, posteromedially retropharyngeal space, laterally above the leve
Read more

Pleomorphic Adenoma of the Tongue Base: A Case Report-Juniper publishers

Image
JUNIPER PUBLISHERS-OPEN ACCESS JOURNAL OF HEAD NECK & SPINE SURGERY Abstract An 86-year-old woman underwent bronchoscopy after developing aspiration pneumonia. She was found to have a tumor of the tongue base and was referred to our department. Fiberscopy revealed a pendulous mass at the tongue base. On computed tomography, a smooth pendulous mass (2cm × 1.7cm) was seen at the base of the tongue, with no deep invasion. The biopsy report indicated possible mucoepidermoid carcinoma. The risk of surgery was high due to her age and co-morbidities, so the patient and her family did not agree to resection of the tumor. Aspiration pneumonia recurred several times over several months, after which she could not take anything orally and became bedridden for weeks. To improve her quality of life by minimally invasive surgery, the tumor was excised transorally under general anesthesia. The pathological diagnosis was pleomorphic adenoma, and the surgical margins were negative
Read more

Chiari Malformation Type III with Good Outcome: Case-Report and Review of Clinical and Radiological Findings-Juniper publishers

Image
JUNIPER PUBLISHERS-OPEN ACCESS JOURNAL OF HEAD NECK & SPINE SURGERY Abstract Chiari III malformation, one of the rare variants of Chiari malformations, is including a small dysplastic posterior fossa, hydrocephalus, medullary abnormalities, and hindbrain herniation into a low occipital/high cervical encephalocele. This type can be lethal if not treated and is related to severe neurological deficits, so surgical care should immediately be undertaken. We are presenting a 1.5-month-old male infant with Chiari III malformation that was managed surgically with good outcome in addition, review the radiological, clinical and pathogenesis of Chiari III malformation. Introduction Type III Chiari malformation is a very rare condition that is described by Chiari in 1891.This type of Chiari defined as hindbrain herniation into a high cervical encephalocele or low occipital, and osseous defects with features of type II Chiari malformation (including a small posterior fo
Read more